Dyke Davidoff Masson syndrome: rare cause of hemiparesis
DOI:
https://doi.org/10.18203/2349-3291.ijcp20253498Keywords:
Dyke Davidoff Masson Syndrome, Hemiparesis, Vascular insult, Gliosis, Cystic encephalomalaciaAbstract
Dyke-Davidoff-Masson syndrome (DDMS) is a rare clinical entity caused by a neurological disorder that results from cerebral injury in -utero or in early infancy resulting in unilateral brain atrophy. The resulting clinical presentation is with hemiplegia, seizures, developmental delay and behavioural disorders. Our case is a 12-year-old boy who presented with hemiparesis, poor scholastic performance and seizures. The MRI brain revealed a decreased volume of the right cerebral hemisphere with gliotic change in the frontal region. The right cerebral peduncle appeared small in size with cystic encephalomalacia and thinning of the corpus callosum. MRI findings were suggestive of DDM syndrome. The electroencephalogram was abnormal. An early recognition will help reduce disability with physiotherapy and anticonvulsant therapy.
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Rondão MBA, Hsu BRRHS, Centeno RS, de Aguiar PHP. Dyke-Davidoff-Masson Syndrome: Main clinical and radiological findings- systematic literature review. Seizure. 2023;110:58-68. DOI: https://doi.org/10.1016/j.seizure.2023.04.020
Al Hatmi A, Almashaikhi T, Al Ajmi E. Imaging Features of Dyke-Davidoff-Masson Syndrome. Sultan Qaboos Univ Med J. 2023;23(1):122-4. DOI: https://doi.org/10.18295/squmj.9.2022.055
Arora R, Rani JY. Dyke-Davidoff-Masson syndrome: imaging features with illustration of two cases. Quant Imaging Med Surg. 2015;5(3):469-71.
Lim S, Westover C, Ratan RB, Guiahi M. Routine abortion training matters for obstetrics and gynecology residents. Open J Obstet Gynecol 2013;03(10):727–31. DOI: https://doi.org/10.4236/ojog.2013.310134
Shrestha B. Acquired cerebral hemiatrophy: Dyke-Davidoff-Masson syndrome—a case report. Turk Neurosurg. 2011;23(1):117–21. DOI: https://doi.org/10.5137/1019-5149.JTN.4283-11.1
Holmes GL. Effect of seizures on the developing brain and cognition. Semin Pediatr Neurol. 2016;23:120–6. DOI: https://doi.org/10.1016/j.spen.2016.05.001
Abdul Rashid AM, Md Noh MSF. Dyke-Davidoff-Masson syndrome: a case report. BMC Neurol. 2018;18(1):76. DOI: https://doi.org/10.1186/s12883-018-1079-3
Behera MR, Patnaik S, Mohanty AK. Dyke-Davidoff-Masson syndrome. J Neurosci Rural Pract. 2012;3(3):411–3. DOI: https://doi.org/10.4103/0976-3147.102646
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