From prenatal diagnosis to postnatal stability: a case of isolated type II congenital pulmonary airway malformation

Swapnil Dadmal; Shubham Kamble; Shilpa P. V.; Smita Jategaonkar; Manish Jain

doi:10.18203/2349-3291.ijcp20252978

Authors

Swapnil Dadmal Department of Paediatrics, MGIMS, Sevagram, Maharashtra, India https://orcid.org/0009-0006-0220-7322
Shubham Kamble Mahatma Gandhi Institute of Medical Sciences, Sevagram https://orcid.org/0000-0003-3812-6760
Shilpa P. V. Department of Paediatrics, MGIMS, Sevagram, Maharashtra, India https://orcid.org/0009-0007-5220-3175
Smita Jategaonkar Department of Paediatrics, MGIMS, Sevagram, Maharashtra, India https://orcid.org/0000-0002-8171-8326
Manish Jain Department of Paediatrics, MGIMS, Sevagram, Maharashtra, India https://orcid.org/0000-0001-6247-5114

DOI:

https://doi.org/10.18203/2349-3291.ijcp20252978

Keywords:

Congenital pulmonary airway malformation, Congenital cystic adenomatoid malformation, Alveolar developmental abnormality, Stocker’s classification

Abstract

Congenital pulmonary airway malformation (CPAM) is the most common congenital lung anomaly. CPAM is characterized by multiple cysts of varying diameter, of embryological origin. With advances in prenatal imaging, it is frequently detected antenatally. We report a male neonate with antenatal diagnosis of CPAM in the lungs at 22 weeks of gestation. The baby was delivered at 39 weeks via planned cesarean section, weighing 2425 gm, and had mild transient tachypnea after birth. Postnatal imaging confirmed multiple thin-walled cysts in the right lung, without compression of adjacent structures. No associated anomalies were found. The neonate was managed conservatively and discharged with multidisciplinary follow-up. This case highlights the possibility of a benign course in asymptomatic CPAM type II, underscores the role of prenatal and postnatal imaging, and discusses current controversies regarding conservative versus surgical management.

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Author Biography

Swapnil Dadmal, Department of Paediatrics, MGIMS, Sevagram, Maharashtra, India

Junior Resident, Department of Paediatrics, MGIMS, Sevagram, Maharashtra, India

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