Enthesitis related arthritis with systemic features

Authors

  • S. Bhavana Department of Clinical Immunology and Rheumatology, ESIC Medical College, Hyderabad, Telangana, India
  • Vijaya Prasanna Parimi Department of Clinical Immunology and Rheumatology, ESIC Medical College, Hyderabad, Telangana, India
  • R. N. Tejaswini Department of Clinical Immunology and Rheumatology, ESIC Medical College, Hyderabad, Telangana, India
  • G. Narsimulu

DOI:

https://doi.org/10.18203/2349-3291.ijcp20251884

Keywords:

Enthesitis-related arthritis, Juvenile idiopathic arthritis, Enthesitis, HLA-B27

Abstract

Systemic juvenile idiopathic arthritis (SJIA), classified as a form of juvenile arthritis, constitutes around 10-20% of all cases of JIA, and is the most common form of arthritis in children. It has no sex predilection and affects children as young as one year of age. Enthesitis occurs in a form of JIA known as enthesitis-related arthritis (ERA), which has a male predilection and is associated with the HLA-B27 allele. Systemic features do not characterize it. We describe a rare presentation of systemic inflammation in ERA in a female child.

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References

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Published

2025-06-25

How to Cite

Bhavana, S., Parimi, V. P., Tejaswini, R. N., & Narsimulu, G. (2025). Enthesitis related arthritis with systemic features. International Journal of Contemporary Pediatrics, 12(7), 1240–1242. https://doi.org/10.18203/2349-3291.ijcp20251884

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Section

Case Reports