Enthesitis related arthritis with systemic features
DOI:
https://doi.org/10.18203/2349-3291.ijcp20251884Keywords:
Enthesitis-related arthritis, Juvenile idiopathic arthritis, Enthesitis, HLA-B27Abstract
Systemic juvenile idiopathic arthritis (SJIA), classified as a form of juvenile arthritis, constitutes around 10-20% of all cases of JIA, and is the most common form of arthritis in children. It has no sex predilection and affects children as young as one year of age. Enthesitis occurs in a form of JIA known as enthesitis-related arthritis (ERA), which has a male predilection and is associated with the HLA-B27 allele. Systemic features do not characterize it. We describe a rare presentation of systemic inflammation in ERA in a female child.
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References
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