Spontaneous CSF otorrhea in cases of Mondini’s dysplasia: a rare cause of recurrent bacterial meningitis

Ameya Bihani, Keya Shah, Priyanka Hardikar, Yogesh Dokhe, Jyoti Dabholkar

Abstract


Inner ear anomaly is rare developmental anomaly with Mondini’s dysplasia being the most common. The perilymphatic fistula cause due to high pressure condition in anomalous inner ear result into CSF otorrhea which become a tract for bacteria to reach central nervous system and cause recurrent meningitis. We are presenting 3 cases of Mondini’s dyaplasia which had CSF leaking into middle ear cleft which was diagnosed with HRCT of temporal bone with cisternography and MRI cisternography and were managed successfully with surgical repair by trans-mastoid approach.


Keywords


Mondini’s dysplasia, Spontaneous CSF otorrhea, Recurrent meningitis

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References


Yogev R. Recurrent meningitis. In: Long SS, Pickering LK, Prober CG, eds. Principles and Practise of Pediatric Infectious Diseases. 3rd ed. Philadelphia, Pa, USA: Churchill Livingstone; 2008.

Tebruegge M, Curtis N. Epidemiology, etiology, pathogenesis, and diagnosis of recurrent bacterial meningitis. Clin Microbiol Rev. 2008;21(3):519-37.

Janocha-Litwin J, Simon K. Recurrent meningitis: a review of current literature. Przegląd Epidemiologiczny. 2013;67(1):41-5.

Victor G, Ruth G. Hereditory congenital ear syndromes. In: Victor Good Hill eds. Diseases, Deafness and Dizziness. 1st ed. Maryland: Harper & Row Publishers: 1990: 591-621.

Griffith AJ, Telian SA, Downs C, Gorski JL, Gebarski SS, Lalwani AK, et al. Familial Mondini dysplasia. Laryngoscope. 1998;108:1368-73.

Arellano B, Ramírez Camacho R, García Berrocal JR, Villamar M, del Castillo I, Moreno F. Sensorineural hearing loss and Mondini dysplasia caused by a deletion at locus DFN3. Arch Otolaryngol Head Neck Surg. 2000;126:1065-9.

Kim L, Wisely CE, Dodson EE. Transmastoid approach to spontaneous temporal bone cerebrospinal fluid leaks: hearing improvement and success of repair. Otolaryngol Head Neck Surg. 2014;150(3):472-8.

Kepenekli-Kadayifci E, Karaaslan A, Atıcı S, Binnetoğlu A, Sarı M, Soysal A, et al. Recurrent bacterial meningitis in a child with Mondini dysplasia. Case Rep Pediatr. 2014;2014:364657.