Spontaneous CSF otorrhea in cases of Mondini’s dysplasia: a rare cause of recurrent bacterial meningitis


  • Ameya Bihani Department of ENT, KEM Hospital, Mumbai, Maharashtra, India
  • Keya Shah Department of ENT, KEM Hospital, Mumbai, Maharashtra, India
  • Priyanka Hardikar Department of ENT, KEM Hospital, Mumbai, Maharashtra, India
  • Yogesh Dokhe Department of ENT, KEM Hospital, Mumbai, Maharashtra, India
  • Jyoti Dabholkar Department of ENT, KEM Hospital, Mumbai, Maharashtra, India


Mondini’s dysplasia, Spontaneous CSF otorrhea, Recurrent meningitis


Inner ear anomaly is rare developmental anomaly with Mondini’s dysplasia being the most common. The perilymphatic fistula cause due to high pressure condition in anomalous inner ear result into CSF otorrhea which become a tract for bacteria to reach central nervous system and cause recurrent meningitis. We are presenting 3 cases of Mondini’s dyaplasia which had CSF leaking into middle ear cleft which was diagnosed with HRCT of temporal bone with cisternography and MRI cisternography and were managed successfully with surgical repair by trans-mastoid approach.


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