Mermaid baby or sirenomelia: a lethal congenital anomaly

Authors

  • Ram Jeewan Singh Department of Pediatric Surgery, All India Institute of Medical Sciences, Patna, Bihar, India
  • Bijay Kumar Suman Department of Pediatric Surgery, All India Institute of Medical Sciences, Patna, Bihar, India
  • Keerthana Bachala Department of Pediatric Surgery, All India Institute of Medical Sciences, Patna, Bihar, India
  • Amit Kumar Department of Pediatric Surgery, All India Institute of Medical Sciences, Patna, Bihar, India
  • Rashi Rashi Department of Pediatric Surgery, All India Institute of Medical Sciences, Patna, Bihar, India
  • Amit Kumar Sinha Department of Pediatric Surgery, All India Institute of Medical Sciences, Patna, Bihar, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20231152

Keywords:

Caudal regression syndrome, Fused lower limb, Mermaid syndrome, Sirenomelia

Abstract

Mermaid syndrome is a very rare, lethal congenital anomaly. It is associated with other congenital anomalies and is incompatible with life. Typical clinical features are fused lower limb from perineum to ankle and single umbilical artery. Etiology is multifactorial and is extreme form of caudal regression syndrome.  When diagnosed in early gestation, termination of pregnancy may be considered.

References

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Published

2023-04-27

Issue

Section

Case Reports