Inflammatory myofibroblastic tumour of an unusual site in an infant
Keywords:Infant, Mesenchymal tumor, Sinus cavity
Inflammatory myofibroblastic tumors are rare mesenchymal tumors of intermediate malignant potential, usually seen in the first or second decades of life. They have a high local recurrence rate but rarely metastasize. The involvement of paranasal sinuses or the nasal cavity is relatively uncommon, especially in infants. In children, there is a predilection for the abdominal cavity and it is rare in infants. Complete surgical excision is the treatment of choice. We report a case of a 10-month-old girl with an inflammatory myofibroblastic tumor of the left nasal cavity and sinuses who was initially treated with chemotherapy in view of the complicated surgical process and later underwent near-total resection as she was not responding to chemotherapy. Knowledge of such tumors among physicians and ENT surgeons will improve the prognosis, as completely excised tumors have a very low recurrence rate and adjuvant therapy may not be needed.
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