Published: 2022-10-27

A case of Ebstein’s anomaly

Sourabh Goswami, Surender Deora, Shubham Kumar, Vivek Mohanty, Rahul Gudhage


Ebstein’s anomaly (EA) is a rare congenital heart disease. It has varied clinical presentation depending upon the spectrum of deformation and function of the tricuspid valve and other structures. A comprehensive evaluation by non- invasive modalities is required for optimal decision making regarding the approach to surgical correction of the disease.


EA, Tricuspid valve, ECG

Full Text:



Hoffman JI, Kaplan S. The incidence of congenital heart disease. J Am Coll Cardiol. 2002;39:1890-900.

Ebstein W. Über einen sehr seltenen Fall von Insufficienz der Valvula tricuspidalis, bedingt durch eine angeborene hochgradige Missbildung derselben. Archiv für Anatomie, Physiologie und wissenschaftliche Medicin. Leipzig. 1866;238-54.

Vlismas PP, Jorde UP, Sims DB. Himalayan P Waves, Alpine A Waves. Circ Heart Fail. 2019;12(10):e006235.

Shaddy RE, Penny DJ, Feltes TF, Cetta F, Mital S. Moss and Adams' heart disease in infants, children, and adolescents: Including the fetus and young adult: Wolters Kluwer, 10th ed. 2022.

Celermajer D, Bull C, Till J. Ebstein's anomaly: Presentation and outcome from fetus to adult. J Am Coll Cardiol. 1994;23(1):170-6.

Celermajer DS, Cullen S, Sullivan ID, Spiegelhalter DJ, Wyse RK, Deanfield JE. Outcome in neonates with Ebstein's anomaly. J Am Coll Cardiol. 1992;19(5):1041-6.

Shiina A, Seward JB, Edwards WD, Hagler DJ, Tajik AJ. Two-dimensional echocardiographic spectrum of Ebstein’s anomaly: Detailed anatomic assessment. J Am College Cardiol. 1984;3:356-70.