A rare case of an Omphalocele Major with associated Tetralogy of Fallot in a newborn

Authors

  • Dharmendra K. Shah Department of Surgery, Medical College Baroda and SSG Hospital, Vadodara, Gujarat, India
  • Shivani R. Chaudhary Department of Surgery, Medical College Baroda and SSG Hospital, Vadodara, Gujarat, India http://orcid.org/0000-0003-4128-1438
  • Margi A. Shah Medical College Baroda and SSG Hospital, Vadodara, Gujarat, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20222431

Keywords:

Omphalocele, Abdominal wall defect, Neonate

Abstract

Omphalocele major (OM) is a surgically challenging condition which owing to its large defect size and other congenital anomalies, is associated with poor outcomes. Complications while managing it are not uncommon. But here, we report a case of OM in a neonate who was successfully managed in a multidisciplinary approach by a team of neonatologist, surgeons and anesthetist.

Author Biographies

Dharmendra K. Shah, Department of Surgery, Medical College Baroda and SSG Hospital, Vadodara, Gujarat, India

Additional Professor,

Head of the unit,

Department of General Surgery

Shivani R. Chaudhary, Department of Surgery, Medical College Baroda and SSG Hospital, Vadodara, Gujarat, India

Senior Resident,

Department of Surgery

Margi A. Shah, Medical College Baroda and SSG Hospital, Vadodara, Gujarat, India

Undergraduate Student M.B.B.S

References

Anyanwu LC, Ade-Ajayi N, Rolle U. Major abdominal wall defects in the low- and middle-income setting: current status and priorities. Pediatr Surg Int. 2020;36(5):579-90.

Seymour NE, Bell RL. Abdominal Wall, Omentum, Mesentery, and Retroperitoneum In: Brunicardi F, Andersen DK, Billiar TR, Dunn DL, Hunter JG, Matthews JB, Pollock RE, editors. Schwartz's Principles of Surgery. McGraw Hill. 2015.

Bilal R, Rustemov D, Sakuov Z, Ibraimov B and Kozhakhmetov A. Case Report: A Rare Case of a Combination of Omphalocele with Umbilical Teratoma. Front Pediatr. 2021;9:726593.

Nolan HR, Wagner ML, Jenkins T, Lim FY. Outcomes in the Major omphalocele population: A single center comprehensive experience. J Pediatr Surg. 2020;55(9):1866-71.

Bauman B, Stephens D, Gershone H, Bongiorno C, Osterholm E, Acton R, Hess D, Saltzman D, Segura B. Management of Major omphaloceles: A systematic review of methods of staged surgical vs. nonoperative delayed closure. J Pediatr Surg. 2016;51(10):1725-30.

van Eijck FC, Aronson DA, Hoogeveen YL, Wijnen RMH. Past and current surgical treatment of Major omphalocele: outcome of a questionnaire sent to authors. 2011;46(3):488.

Puri B, Sreevastava DK. Exomphalos Defects: A Review of 15 Cases. Med J Armed Forces India. 2008;64(2):115-8.

Vachharajani AJ, Rao R, Keswani S, Mathur AM. Outcomes of exomphalos: an institutional experience. Pediatr Surg Int. 2009;25(2):139-44.

Akinkuotu AC, Sheikh F, Olutoye OO, Lee TC, Fernandes CJ, Welty SE, Ayres NA, Cass DL. Giant omphaloceles: surgical management and perinatal outcomes. J Surg Res. 2015;198(2):388-92.

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Published

2022-09-26

Issue

Section

Case Reports