Rare association of obstructed supracardiac total anomalous pulmonary venous connection with coarctation of aorta: case report
DOI:
https://doi.org/10.18203/2349-3291.ijcp20221387Keywords:
Total anomalous pulmonary venous connection, Coarctation of aorta, Congenital heart diseaseAbstract
Coexistence of TAPVC (total anomalous pulmonary venous connection) and coarctation of aorta rarely occurs. Newborn weighing 2.4 kg admitted in Sangli civil hospital NICU with respiratory distress with cyanosis. Chest X-ray of baby was suggestive of ground glass appearance of bilateral lung fields and cardiomegaly. SpO2 of baby was fluctuating between 85 to 90% on nasal CPAP. 2D echo showed baby was having obstructed supracardiac TAPVC with severe discrete post-ductal coarctation of aorta. There was stretched PFO shunting R-L and small PDA shunting R-L. Baby was planned for emergency surgery but couldn’t make it to operation theatre and succumbed within 30 hours of life. Till now there are very few case reports of TAPVC with coarctation but no case of obstructed supracardiac TAPVC with coarctation has been reported.References
Doksöz Ö, Güven B, Demirpençe S. Coarctation of the aorta with infracardiac total anomalous pulmonary venous drainage: a rare combination. Ann Thorac Cardiovasc Surg. 2014;20:778-80.
de Leval MR, Stark J B-CR. Total anomalous pulmonary venous drainage to superior vena cava associated with preductal coarctation of aorta. Successful correction in a 12-day-old infant. Br Hear J. 1973;35:1098-03.
Seale AN, Uemura H, Webber SA. Total anomalous pulmonary venous connection: morphology and outcome from an international population-based study. Circulation. 2010;(122):2718-26.
Hayashi H, Sughimoto K, Oka N, Tsuchida Y MK. Coarctation of the aorta with total anomalous pulmonary venous connection: a case report. AME Case Rep. 2021;5:11.
