Published: 2022-02-23

Mauriac syndrome; a rare complication of type 1 diabetes mellitus

Anagha Ravi, Naresh Meena


Mauriac syndrome is a rare complication of poorly controlled Type 1 diabetes mellitus.It is characterized by, truncal obesity, delayed puberty, cushingoid features, hepatomegaly. Although rare in developed countries, cases are seen in developing countries like India due to lack of awareness and poor socio-economic status. We report a case of 5 years old male child with type 1 diabetes mellitus and poor glycemic control with features of Mauriac syndrome from Jhalawar district, Rajasthan.


Mauriac syndrome, Type I diabetes mellitus, Hepatomegaly, Rare complication

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