Dyke Davidoff Masson syndrome: a rare cause of cerebral hemiatrophy in 11 months old

Authors

  • Amit Vatkar Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India
  • Ipsita Vashishtha Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India
  • Vinaykumar P. Hedaginal Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India
  • B. Revanth Sai Madhav Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20205528

Keywords:

Dyke-Davidoff-Masson syndrome, Hemiatrophy, Spastic hemiplegia

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) is an uncommon condition, characterized radiologically by cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses, of unknown frequency resulting from brain injury due to large no of causes; especially in early life. Mostly presents early in life with seizures, learning difficulty, contralateral hemiparesis and facial symmetry. Here we present a case of 11 months old female child with developmental delay, visual abnormality, microcephaly and spastic hemiplegia. CT-brain done which was suggestive of infantile type of cerebral hemiatrophy or DDMS.

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Author Biographies

Amit Vatkar, Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India

Department of Paediatrics, Assistant Professor

Ipsita Vashishtha, Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India

Department of Paediatrics, Junior resident

Vinaykumar P. Hedaginal, Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India

Department of Paediatrics, Junior Resident

B. Revanth Sai Madhav, Department of Paediatrics, DY Patil University, School of medicine, Navi Mumbai, Maharashtra, India

Department of Paediatrics, Junior Resident

References

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Published

2020-12-23

How to Cite

Vatkar, A., Vashishtha, I., Hedaginal, V. P., & Madhav, B. R. S. (2020). Dyke Davidoff Masson syndrome: a rare cause of cerebral hemiatrophy in 11 months old. International Journal of Contemporary Pediatrics, 8(1), 187–189. https://doi.org/10.18203/2349-3291.ijcp20205528

Issue

Section

Case Reports