Case of congenital diastematomyelia type 1: a rare presentation

Balaji M. D., Shivaprakash N. C., Prashanth Kumar Thangella


Diastematomyelia is a rare congenital anomaly that results in the splitting of the spinal cord in a longitudinal (sagittal direction). It is also known as a split cord malformation, refers to a type of spinal dysraphism (spina bifida occulta) when there is a longitudinal split in the spinal cord. We report a case of new born female baby with Diastematomyelia type 1 associated with low lying conus, tethered cord and dorsal dermal sinus.


Diastematomyelia, Tethered cord, MRI Scan

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