Severe haemoptysis in a 5 year old child with Kartagener’s syndrome: case report

Mohinish S.; Mallesh K.; Prashanth H. K.; Ravichandra K. R.

doi:10.18203/2349-3291.ijcp20200130

Authors

Mohinish S. Department of Pediatrics, Bangalore Medical College and Research Institute, Bangalore, Karnataka, India
Mallesh K. Department of Pediatrics, Bangalore Medical College and Research Institute, Bangalore, Karnataka, India
Prashanth H. K. Department of Pediatrics, Bangalore Medical College and Research Institute, Bangalore, Karnataka, India
Ravichandra K. R. Department of Pediatrics, Bangalore Medical College and Research Institute, Bangalore, Karnataka, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20200130

Keywords:

Absent bronchus, Dextrocardia, Haemoptysis, Kartagener`s syndrome, Primary ciliary dyskinesia, Short neck

Abstract

Kartagener`s syndrome, a rare autosomal recessive disorder is a type of Primary Ciliary Dyskinesia (PCD) associated situs inversus, bronchiectasis, sinusitis and male infertility. We present a case of a 5-year-old girl who came with features of bilateral glue ear, recurrent sinusitis, recurrent hemoptysis and dextrocardia. She was diagnosed to have Kartagener`s syndrome and was evaluated for recurrent hemoptysis.

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