DOI: http://dx.doi.org/10.18203/2349-3291.ijcp20192793

Unna Thost syndrome: a case report

Geetha M., Rajeswari Bhat, Kiran B., Madhusmitha Jena, Libni D. Angel

Abstract


Unna thost syndrome is Palmo Plantar Keratoderma (PPK) of diffuse non epidermolytic type inherited in autosomal dominant fashion. Authors had a seven-year-old boy born to second degree consanguineous parents had palmoplantar keratoderma with hyperhidrosis with positive family history. He was promptly diagnosed and treated with acitretin and showed improvement.


Keywords


Hyperhidrosis, Epidermolysis, Palmo plantar keratoderma, Unna Thost Syndrome, Vorner

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References


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