Supratentorial atypical teratoid/rhabdoid tumor: a case report

Jyoti K. Kudrimoti, Neeta A. Wahane, Shailja C. Puranik


Atypical teratoid rhabdoid tumor (ATRT) is a rare and highly aggressive malignant tumor of infancy and childhood with fatal outcome. Common site is kidney, but it can also occur in the liver, thymus and the CNS. The supratentorial compartment is less frequently the primary site for this neoplasm, but cases arising from the cerebral hemisphere have also been reported. Study came across a case of 18 months female child who presented with convulsions and MRI showed right frontal space occupying lesion, which after IHC confirmed as ATRT.


ATRT, Diagnosis

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