Massive hepatomegaly in a neonate: an unusual cause

Authors

  • Ritika Khurana Department of Pediatrics, University College of Medical sciences and Guru Tegh Bahadur Hospital, Garden, Delhi, India
  • Anju Aggarwal Department of Pediatrics, University College of Medical sciences and Guru Tegh Bahadur Hospital, Garden, Delhi, India
  • Aashima Dabas Department of Pediatrics, University College of Medical sciences and Guru Tegh Bahadur Hospital, Garden, Delhi, India
  • Natasha Gupta Department of Radiodiagnosis, University College of Medical sciences and Guru Tegh Bahadur Hospital, Garden, Delhi, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20164618

Keywords:

Hepatomegaly, Neonate, Neuroblastoma 4S

Abstract

A female neonate presented with progressive abdominal distension. Liver was palpable, 11 cm below costal margin and a spleen of 10 cm. USG abdomen revealed massive hepatomegaly with multiple nodules in liver, kidney size and texture being normal. Contrast enhanced CT scan of the abdomen was suggestive of enlarged multinodular liver with splenomegaly. Liver biopsy revealed replacement of liver architecture by small rounded cells, which were positive for synaptophysin and S100 stains suggestive of neuroblastoma. A repeat abdominal radiological evaluation revealed a small 2 x 1 cm mass in left suprarenal area. Neuroblastoma stage 4S presenting as hepatomegaly is rare.

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References

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Published

2016-12-21

How to Cite

Khurana, R., Aggarwal, A., Dabas, A., & Gupta, N. (2016). Massive hepatomegaly in a neonate: an unusual cause. International Journal of Contemporary Pediatrics, 4(1), 274–275. https://doi.org/10.18203/2349-3291.ijcp20164618

Issue

Vol. 4 No. 1 (2017): January-February 2017

Section

Case Reports
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