Impact of education on the knowledge and skills of parents of children with sickle cell disease


  • Purnima Yadav Department of Paediatrics, Jawaharlal Nehru medical college, DMIMSU Wardha, Maharashtra, India
  • Jayant Vagha Department of Paediatrics, Jawaharlal Nehru medical college, DMIMSU Wardha, Maharashtra, India



Education of parents, OSCE, Sickle cell disease


Background: Sickle cell disease is a haemoglobinopathy that affects millions throughout the world. It leads to poor quality of the life and increased mortality in children and young adults. In Vidarbha, SCD is common and it is pathetic to see children in morbid state dying due to some or the other crisis. Parents must be educated about the nature of the disease, earliest signs of crises and seek help, treat all febrile illnesses promptly. We contemplated that the key to success in the management of such children is parental education and this prompted us to undertake the present study.

Methods: It was interventional study, done in Pediatric SCD clinic done in 2 years. Parent’s preexisting knowledge and awareness about sickle cell disease was assessed with the help of questionnaire and OSCE. They were then educated with the help of educational module comprising of pamphlets in Marathi, pictures, and also trained in clinical examination of their child to detect pallor, fever, jaundice, respiratory distress, pulse and splenic enlargement. After intervention posttest and OSCE was conducted again.

Results: The pre-existing knowledge about inheritance, signs and symptoms of sickle cell anemia was high, but parents showed lack in skills of assessment of crises. These skills improved significantly after intervention. There was statistically significant (p<0.05) difference between average pretest and post test scores of each skill tested.

Conclusions: Modular teaching using OSCE helps in improving skills of parents for early detection of sickle cell crises.


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