Linear nevus sebaceous syndrome with lissencephaly
DOI:
https://doi.org/10.18203/2349-3291.ijcp20162399Keywords:
Lissencephaly, Hemimegalencephaly, Linear nevus sebaceous syndromeAbstract
Linear nevus sebaceous syndrome is a congenital neurocutaneous syndrome comprising of nevus sebaceous, seizures and mental retardation. We report a 6 month old female child with a linear nevus sebaceous over the face and scalp, whose brain imaging revealed ipsilateral lissencephaly with hemimegalencephaly. Lissencephaly is rarely reported in this syndrome.
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