An unusual association: duodenal atresia and situs inversus incompletes-a case report and discussion

Fatima Al Zahra; Nasir Aziz Khan; Nadeem Akhtar

doi:10.18203/2349-3291.ijcp20221084

Authors

Fatima Al Zahra Department of Paediatric Surgery, Pakistan Institute of Medical Sciences, Islamabad, Pakistan
Nasir Aziz Khan Department of Paediatric Surgery, Quaid e-Azam International Hospital, Islamabad, Pakistan
Nadeem Akhtar Department of Paediatric Surgery, Pakistan Institute of Medical Sciences, Islamabad, Pakistan

DOI:

https://doi.org/10.18203/2349-3291.ijcp20221084

Keywords:

Atresia, Duodenum, Syndrome, Situs inversus

Abstract

Coming across a number of duodenal atresia in daily practice any paediatric surgeon may conclude that it’s one of the most technically challenging small gut atresia with variations of pathology that has an incidence of 1 in 4000 or 5000 live births. It has marked association with a number of conditions like downs syndrome (trisomy 21) being on crest, accounting for 20-40% of cases. Other prominent associations include VACTERL (vertebral, anotectal malformation, cardiac, tracheo esophageal, renal, limb) anomalies, concurrent other small gut atresias, preduodenal portal vein. A relatively rare association we have come across recently has been situs transverus co existing with duodenal atresia that prompted us to rummage through literature for similar cases embarking us to publish our own finding as very little has been said so far in this regard.

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References

Kimura K, Loening-Baucke V. Bilious vomiting in the newborn: rapid diagnosis of intestinal obstruction. Am Fam Phys. 2000;61(9):2791-8.

Buchin PJ, Levy JS, Schullinger JN. Down's syndrome and the gastrointestinal tract. J Clin Gastroenterol. 1986;8(2):111-4.

LeWald LT. Complete transposition of the viscera: A report of twenty-nine cases, with remark on etiology. JAMA. 1925;84(4):216-68.

Casey B. Genetics of human situs abnormalities. Am J Med Genet. 2001;101(4):356-8.

Lee SE, Kim HY, Jung SE, Lee SC, Park KW, Kim WK. Sites anomalies and gastrointestinal abnormalities. J Pediatr Surg. 2006;41(7):1237-42.

Adeyemi SD. Combination of annular pancreas and partial situs inversus: a multiple organ malrotation syndrome associated with duodenal obstruction. J Pediatr Surg. 1988;23(2):188-91.

Nawaz A, Matta H, Hamchou M, Jacobez A, Trad O, AlSalem AH. Situs inversus abdominus in association with congenital duodenal obstruction: a report of two cases and review of the literature. Pediatr Surg Int. 2005;21(7):589-92.

Akel S, Halabi J, Shamis R. Abdominal situs inversus with congenital duodenal stenosis: Rare association. Eur J Pediatr Surg. 1998;8(1):55-7.

Mohebi M, Moghaddam H, Horri M. Congenital heart defects in children with dextrocardia: a ten-year study. Int J Pediatr. 2019;7(1):8815-20.

Sayuti KA, Shamsuddin AM, Mamat AZ, Zain MRM, Ramli N, Mokhtar AM, et al. (2021). Right-sided patent ductus arteriosus with bovine aortic arch, tetralogy of Fallot, dextrocardia and situs inversus. J Surg Case Rep. 2021;7:307.