Case of congenital diastematomyelia type 1: a rare presentation

Authors

  • Balaji M. D. Department of Pediatrics, Adichunchanagiri Institute of Medical Sciences, B.G nagara, Nagamangala taluk, Mandya District, Karnataka, Pincode -571448, India
  • Shivaprakash N. C. Department of Pediatrics, Adichunchanagiri Institute of Medical Sciences, B.G nagara, Nagamangala taluk, Mandya District, Karnataka, Pincode -571448, India
  • Prashanth Kumar Thangella Department of Pediatrics, Adichunchanagiri Institute of Medical Sciences, B.G nagara, Nagamangala taluk, Mandya District, Karnataka, Pincode -571448, India

DOI:

https://doi.org/10.18203/2349-3291.ijcp20160176

Keywords:

Diastematomyelia, Tethered cord, MRI Scan

Abstract

Diastematomyelia is a rare congenital anomaly that results in the splitting of the spinal cord in a longitudinal (sagittal direction). It is also known as a split cord malformation, refers to a type of spinal dysraphism (spina bifida occulta) when there is a longitudinal split in the spinal cord. We report a case of new born female baby with Diastematomyelia type 1 associated with low lying conus, tethered cord and dorsal dermal sinus.

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Published

2016-12-31